Case for diagnosis. Erythroderma as manifestation of hypereosinophilic syndrome
An. bras. dermatol
;
93(3): 451-453, May-June 2018. tab, graf
Artículo
en Inglés
| LILACS
| ID: biblio-949877
ABSTRACT
Abstract Hypereosinophilic syndrome is defined as persistent eosinophilia (>1500/µL for more than six months) associated with organ involvement, excluding secondary causes. It is a rare, potentially lethal disease that should be considered in cutaneous conditions associated with hypereosinophilia. We report a case of erythroderma as a manifestation of hypereosinophilic syndrome. A 36-year-old male with no comorbidities presented progressive erythroderma, pruritus, peripheral neuropathy, and eosinophilia in the previous seven months. No mutations were found in FIP1L1/PDGFRA. Patient experienced rapid remission in response to oral prednisone and hydroxyurea. Cutaneous manifestations may be the only evidence of hypereosinophilic syndrome. Genotyping excludes myeloproliferative disease, thereby orienting treatment and prognosis.
Texto completo:
Disponible
Índice:
LILACS (Américas)
Asunto principal:
Dermatitis Exfoliativa
/
Síndrome Hipereosinofílico
Tipo de estudio:
Estudio diagnóstico
/
Estudio pronóstico
Límite:
Adulto
/
Humanos
/
Masculino
Idioma:
Inglés
Revista:
An. bras. dermatol
Asunto de la revista:
Dermatologia
Año:
2018
Tipo del documento:
Artículo
País de afiliación:
Brasil
Institución/País de afiliación:
Pontifícia Universidade Católica de São Paulo/BR
/
Universidade Estadual Paulista/BR
Similares
MEDLINE
...
LILACS
LIS