Surgical stabilization of lower limbs in osteogenesis imperfecta using modified sofield-millar operation

ABSTRACT

We present the results of intramedullary rodding of long bones of the lower limbs in children with osteogenesis imperfecta using modified Sofield-Millar operation. Fourteen patients [mean age at primary operation was 5 years 11 months] was treated with modified Sofield-Milar operation which allows minimal bone exposure. preservation of the periosteum and keeping the number of osteotomies to the minimum. Union was achieved in all cases within seven weeks. Of the 14 patients [29 bones] treated with non elongating rods, rod revisions were needed in 13 patients [26 bones]. We found no statistical significant difference between the width of the bone immediately postoperatively and at the final follow up. The walking ability was improved in 4 patients. Advantages of less invasive surgery in osteogenesis imperfecta are rapid bone union, no bone atrophy or non union, better post operative mobility and small scab