Crohn's disease and idiopathic thrombocytopenic purpura in a patient with ectodermal dysplasia and immunodeficiency
Iranian Journal of Allergy, Asthma and Immunology. 2006; 5 (3): 143-145
en Inglés
| IMEMR
| ID: emr-137881
ABSTRACT
In this case report we will describe a rare association between anhyrotic ectodermal dysplasia [AED] and immunodeficiency and autoimmunity [in our case Idiopathic Thrombocytopenic Purpura [ITP] and Crohn disease]. AED is a rare congenital disorder characterized by sparse hair, abnormal teeth and anhidrosis due to lack of eccrine glands. The survey of 87 cases with [AED] revealed only one Irritable Bowel Disease [IBD]. AED has only two relevancies with immunodeficiency [EDA-ID Ectodermal Dysplasia Anhyrotic with Immunodeficiency] and APE-CED [Autoimmune polyendocrinopathy, Candidiasis and Ectodermal Dysplasia] that in our case EDA-ID is strongly suspected
Buscar en Google
Índice:
IMEMR (Mediterraneo Oriental)
Idioma:
Inglés
Revista:
Iran. J. Allergy Asthma Immunol.
Año:
2006
Similares
MEDLINE
...
LILACS
LIS