[Right-sided bochdalek hernia associated with upper limb anomaly]

ABSTRACT

Congenital diaphragmatic hernia is a malformation characterized by herniation of the abdominal contents to the thorax through a defect into the diaphragm. When the abdominal organs enter the chest through such a defect, lung development may be impeded, the heart may be displaced and the vascular structures may be distorted. These alterations cause pulmonary hypoplasia, pulmonary hypertention and cardiac abnormalities resulting in neonatal mortality and morbidity. In this article, we report a right-sided Bochdalek hernia associated with upper exterimity anomalies in a newborn infant with a gestational age of 32 weeks. He died one hour after birth due to respiratory distress. Gross examination revealed hernaition of the liver, small and large intestines into the thorax through a 6 by 6 centimeter foramen in the right hemidiaphragm. Upper exterimity abnormalities included radial deviation of both wrists and internal rotation of left hand