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Report of congenital generalized lipodystrophy in children's medical center, Tehram, Iran
Govaresh. 2005; 10 (4): 241-245
en Inglés | IMEMR | ID: emr-70708
ABSTRACT
Generalized lipodystrophy is a rare disorder in children characterized by absence of subcutaneous adipose tissue. We evaluated 10 patients with generalized lipodystrophy by skin and liver biopsy. Eight patients with steatohepatitis and cirrhosis were treated with Ursobile [uorsodeoxycholic acid] and vitamin E. In follow-up, serum triglyceride level was decreased
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Índice: IMEMR (Mediterraneo Oriental) Asunto principal: Piel / Ácido Ursodesoxicólico / Vitamina E / Preescolar / Estudios Retrospectivos / Lactante / Hígado Tipo de estudio: Informe de Casos Límite: Femenino / Humanos / Masculino Idioma: Inglés Revista: Govaresh Año: 2005

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Índice: IMEMR (Mediterraneo Oriental) Asunto principal: Piel / Ácido Ursodesoxicólico / Vitamina E / Preescolar / Estudios Retrospectivos / Lactante / Hígado Tipo de estudio: Informe de Casos Límite: Femenino / Humanos / Masculino Idioma: Inglés Revista: Govaresh Año: 2005