Hemophagocytic lymphohistiocytosis in a neonate with cutis marmorata telangiectatica congenita
Saudi Medical Journal. 2006; 27 (11): 1751-1753
en Inglés
| IMEMR
| ID: emr-80659
ABSTRACT
In this case report we describe the first case of hemophagocytic lymphohistiocytosis with concurrent cutis marmorata telangiectatica congenita. She had pancytopenia and hepatosplenomegaly, hemophagocytic cells in spleen necropsy, and she died with respiratory failure and pseudomonas induced septicemia
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Índice:
IMEMR (Mediterraneo Oriental)
Asunto principal:
Piel
/
Telangiectasia
/
Médula Ósea
/
Enfermedades Cutáneas Vasculares
/
Linfohistiocitosis Hemofagocítica
Tipo de estudio:
Informe de Casos
Límite:
Femenino
/
Humanos
Idioma:
Inglés
Revista:
Saudi Med. J.
Año:
2006
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