MR and CT imaging in the Dyre-Davidoff-Masson syndrome: report of three cases and contribution to pathogenesis and differential diagnosis
Arq. neuropsiquiatr
; 56(4): 803-7, dez. 1998. ilus
Article
en En
| LILACS
| ID: lil-226022
Biblioteca responsable:
BR1.1
ABSTRACT
Cerebral hemiatrophy of Dyke-Davidoff-Masson syndrome is a condition characterized by seizures, facial asymmetry, contralateral hemiplegia or hemiparesis, and mental retardation. These findings are due to cerebral injury that may occur early in life or in utero. The radiological features are unilateral loss of cerebral volume and associated compensatory bone alterations in the calvarium, like thickening, hyperpneumatization of the paranasal sinuses and mastoid cells and elevation of the petrous ridge. The authors describe three cases. Classical findings of the syndrome are present in variable degrees according to the extent of the brain injury. Pathogenesis is commented.
Texto completo:
1
Índice:
LILACS
Asunto principal:
Convulsiones
/
Encéfalo
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Imagen por Resonancia Magnética
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Tomografía Computarizada por Rayos X
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Asimetría Facial
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Hemiplejía
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Discapacidad Intelectual
Tipo de estudio:
Diagnostic_studies
/
Etiology_studies
Límite:
Adult
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Female
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Humans
Idioma:
En
Revista:
Arq. neuropsiquiatr
Asunto de la revista:
NEUROLOGIA
/
PSIQUIATRIA
Año:
1998
Tipo del documento:
Article