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Blue rubber bleb nevus syndrome
Rodrigues, Daleth; Bourroul, Maria Lucia de Moraes; Ferrer, Ana Paula Scoleze; Monteiro Neto, Henrique; Gonçalves, Manoel Ernesto P; Cardoso, Silvia Regina.
  • Rodrigues, Daleth; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto da Criança.
  • Bourroul, Maria Lucia de Moraes; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto da Criança.
  • Ferrer, Ana Paula Scoleze; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto da Criança.
  • Monteiro Neto, Henrique; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto da Criança.
  • Gonçalves, Manoel Ernesto P; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto da Criança.
  • Cardoso, Silvia Regina; Universidade de Säo Paulo. Faculdade de Medicina. Hospital das Clínicas. Instituto da Criança.
Rev. Hosp. Clin. Fac. Med. Univ. Säo Paulo ; 55(1): 29-34, Jan.-Feb. 2000. ilus
Artículo en Inglés | LILACS | ID: lil-260705
RESUMO
The blue rubber nevus syndrome consists of multiple venous malformations in the skin and gastrointestinal tract associated with intestinal hemorrhage and iron deficiency anemia. Other organs may be involved. The causes of this syndrome are unknown. Its most common presentation is in the form of sporadic cases, but dominant autosomal inheritance has been described. It is a condition that affects both sexes equally, and its occurrence is rare in the black race. We present a case of this syndrome diagnosed in a 11-year-old patient. He had severe anemia and a venous swelling on the trunk. Similar lesions were found in the stomach, bowel, and on his foot. We emphasize the main clinical aspects intestine, eyes, nasopharynx, parotids, lungs, liver, spleen, heart, brain, pleura, peritoneum, pericardium, skeletal muscles, bladder, and penis lesions, systemic complications that may occur to these patients which are thrombosis and calcification, as well as consumptive coagulopathy and thrombocytopenia that may occur within the nevi.
Asunto(s)
Texto completo: Disponible Índice: LILACS (Américas) Asunto principal: Neoplasias Cutáneas / Nevo Azul Tipo de estudio: Estudio diagnóstico Límite: Niño / Humanos / Masculino Idioma: Inglés Revista: Rev. Hosp. Clin. Fac. Med. Univ. Säo Paulo Asunto de la revista: Medicina Año: 2000 Tipo del documento: Artículo

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Texto completo: Disponible Índice: LILACS (Américas) Asunto principal: Neoplasias Cutáneas / Nevo Azul Tipo de estudio: Estudio diagnóstico Límite: Niño / Humanos / Masculino Idioma: Inglés Revista: Rev. Hosp. Clin. Fac. Med. Univ. Säo Paulo Asunto de la revista: Medicina Año: 2000 Tipo del documento: Artículo