Anomalía de Ebstein / Ebstein anomaly

ABSTRACT

We evaluated the results for primary repair of Ebstein anomaly in 61 patients, both adults and children. The records were reviewed of patients undergoing repair of Ebstein anomaly at the Congenital Heart Surgery Service of the National Institute of Cardiology [quot ]Ignacio Chávez[quot ] from January 1993 to August 2003. Functional, demographic, and echocardiographic parameters were studied both preoperatively and postoperatively, along with functional status and adverse events. The repair technique involved vertical plication of the atrialized ventricle and valve leaflet reimplantation after clockwise rotation or replacement of tricuspid valve. Ebstein repair has good functional outcomes in patients despite residual tricuspid regurgitation, likely because of reduction in right ventricular volume loading and relative annular and ventricular plasticity. Intraoperative radiofrequency ablation represents an important adjunctive treatment for intractable arrhythmias, which may now represent relative indications for operative intervention.