Your browser doesn't support javascript.
loading
Clinical and functional evaluation of the joint status of hemophiliac adults at a Brazilian blood center
Ferreira, Adriana Aparecida; Bustamante-Teixeira, Maria Teresa; Leite, Isabel Cristina Gonçalves; Corrêa, Camila Soares Lima; Rodrigues, Daniela de Oliveira Werneck; Cruz, Danielle Teles da.
  • Ferreira, Adriana Aparecida; Universidade Federal de Juiz de Fora. Juiz de Fora. BR
  • Bustamante-Teixeira, Maria Teresa; Universidade Federal de Juiz de Fora. Juiz de Fora. BR
  • Leite, Isabel Cristina Gonçalves; Universidade Federal de Juiz de Fora. Juiz de Fora. BR
  • Corrêa, Camila Soares Lima; Universidade Federal de Juiz de Fora. Juiz de Fora. BR
  • Rodrigues, Daniela de Oliveira Werneck; Universidade Federal de Juiz de Fora. Juiz de Fora. BR
  • Cruz, Danielle Teles da; Universidade Federal de Juiz de Fora. Juiz de Fora. BR
Rev. bras. hematol. hemoter ; 35(1): 23-28, 2013. tab
Artículo en Inglés | LILACS | ID: lil-670455
ABSTRACT

BACKGROUND:

Hemophilia is a potentially disabling condition as hemophilic arthropathy develops early in life and is progressive, especially in patients treated in an on-demand regime.

Objective:

This study aimed to describe the structural joint status and the functional independence score of hemophiliac adults and correlate structural damage with the functional deficits found in these patients.

METHODS:

Hemophiliacs at the Juiz de Fora Regional Blood Center - HEMOMINAS Foundation, aged 18 years and over and treated in an on-demand regime, were clinically evaluated in respect to structural joint damage using the World Federation of Hemophilia Physical Examination Scale (WFH-PE) and functional deficits using the Functional Independence Score in Hemophilia (FISH). The Spearman rank test was used to evaluate the correlation between the two scores.

RESULTS:

Thirty-nine patients were evaluated. The mean age was 36.8 years. Target joints were detected in 69.2% of patients studied. The mean Physical Examination Scale and Functional Independence Score were 16.87 and 25.64, respectively. Patients with mild hemophilia showed no significant joint involvement. Patients with severe or moderate hemophilia had similar results regarding structural damage (p-value < 0.001) and functional deficits (p-value = 0.001). There was statistical significance in the correlation between the two scores (r = -0.850; p-value = 0.01).

CONCLUSIONS:

The World Federation of Hemophilia Physical Examination Scale and Functional Independence Score in Hemophilia may be useful to clinically assess structural joint damage and functional deficits in hemophiliacs as the tools are inexpensive and easy to administer and may be able to detect hemophilic arthropathy, which results from recurrent hemarthrosis and is common in the population studied.
Asunto(s)


Texto completo: Disponible Índice: LILACS (Américas) Asunto principal: Hemofilia B / Evaluación de la Discapacidad / Hemartrosis / Hemofilia A / Artropatías Límite: Adolescente / Adulto / Anciano / Humanos / Masculino País/Región como asunto: America del Sur / Brasil Idioma: Inglés Revista: Rev. bras. hematol. hemoter Asunto de la revista: Hematología Año: 2013 Tipo del documento: Artículo País de afiliación: Brasil Institución/País de afiliación: Universidade Federal de Juiz de Fora/BR

Similares

MEDLINE

...
LILACS

LIS


Texto completo: Disponible Índice: LILACS (Américas) Asunto principal: Hemofilia B / Evaluación de la Discapacidad / Hemartrosis / Hemofilia A / Artropatías Límite: Adolescente / Adulto / Anciano / Humanos / Masculino País/Región como asunto: America del Sur / Brasil Idioma: Inglés Revista: Rev. bras. hematol. hemoter Asunto de la revista: Hematología Año: 2013 Tipo del documento: Artículo País de afiliación: Brasil Institución/País de afiliación: Universidade Federal de Juiz de Fora/BR