Enfermedad de Von Economo: Caso clínico / Lethargic Encephalitis: Report of one case
Rev. méd. Chile
; 141(4): 531-534, abr. 2013. tab
Article
en Es
| LILACS
| ID: lil-680476
Biblioteca responsable:
CL1.1
ABSTRACT
Lethargic encephalitis (LE) is a Central Nervous System disorder following an upper respiratory tract infection, characterized by sleep disturbances, clinical symptoms corresponding to basal ganglia involvement and in some cases, neuropsychiatric sequelae. We report a 18-year-old mole with a history of sinusitis treated with azithromycin, two weeks before, presenting with fever, headache, confusion and myoclonus. Urine analysis was positive for cannabis. Cerebro spinal fluid analysis showed mononuclear pleiocytosis (109xmm³) and an increase in protein concentration ofl.6 g/dl. Forty eight hours after admission, the patient required mechanical ventilation and subsequently a status epilepticus appeared. Ten days later, fever, rigidity and resting tremor appeared. A magnetic resonance imaging showed hyperintensities in FLALR sequence in the right insular cortex. The patient continued with extreme rigidity, catatonia and mutism. Considering the possibility ofa LE, methyl prednisolone 1 g/day was administered for five consecutive days followed by prednisone 40 mgl day, observing a dramatic improvement of rigidity and tremors.
Palabras clave
Texto completo:
1
Índice:
LILACS
Asunto principal:
Enfermedad de Parkinson Posencefalítica
/
Encefalitis
Tipo de estudio:
Health_economic_evaluation
Límite:
Adolescent
/
Humans
/
Male
Idioma:
Es
Revista:
Rev. méd. Chile
Asunto de la revista:
MEDICINA
Año:
2013
Tipo del documento:
Article