Incontinentia pigmenti
An. bras. dermatol
; 89(1): 26-36, Jan-Feb/2014. tab, graf
Article
en En
| LILACS
| ID: lil-703556
Biblioteca responsable:
BR1.1
ABSTRACT
Incontinentia pigmenti is a rare genodermatosis in which the skin involvement occurs in all patients. Additionally, other ectodermal tissues may be affected, such as the central nervous system, eyes, hair, nails and teeth. The disease has a X-linked dominant inheritance pattern and is usually lethal to male fetuses. The dermatological findings occur in four successive phases, following the lines of Blaschko First phase - vesicles on an erythematous base; second phase - verrucous hyperkeratotic lesions; third phase - hyperchromic spots and fourth phase - hypochromic atrophic lesions.
Palabras clave
Texto completo:
1
Índice:
LILACS
Asunto principal:
Piel
/
Incontinencia Pigmentaria
Tipo de estudio:
Etiology_studies
Límite:
Humans
/
Male
Idioma:
En
Revista:
An. bras. dermatol
Asunto de la revista:
DERMATOLOGIA
Año:
2014
Tipo del documento:
Article