Clouston syndrome associated with eccrine syringofibroadenoma
An. bras. dermatol
; 89(3): 504-506, May-Jun/2014. graf
Article
en En
| LILACS
| ID: lil-711619
Biblioteca responsable:
BR1.1
ABSTRACT
Eccrine syringofibroadenoma is a rare benign neoplasia derived from acrosyryngium cells of the eccrine sudoriferous glands. It affects the extremities of elderly individuals as solitary tumors, or may also present as multiple lesions. There are controversies about the pathogenesis and differentiation of the tumor. Eccrine syringofibroadenoma has been associated with subjacent conditions, such as for example, hypohidrotic ectodermic dysplasias. The authors describe a case report of a patient with Clouston Syndrome, who presented papules and nodules in extremities, clinically and histologically compatible with eccrine syringofibroadenoma. There are only three cases described in the literature, associated with Clouston Syndrome, and this is the fourth case.
Palabras clave
Texto completo:
1
Índice:
LILACS
Asunto principal:
Neoplasias de las Glándulas Sudoríparas
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Displasia Ectodérmica
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Fibroadenoma
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Glándulas Ecrinas
Tipo de estudio:
Risk_factors_studies
Límite:
Adult
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Female
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Humans
Idioma:
En
Revista:
An. bras. dermatol
Asunto de la revista:
DERMATOLOGIA
Año:
2014
Tipo del documento:
Article