Diagnostic and therapeutic problems arising from celiac axis pheochromocytoma in a child: a case report

RESUMO

Pheochromocytoma is a rare tumor in childhood. Most patients present with sustained hypertension (80%), and 50% of these tumors are bilateral, multiple or extraadrenal. An increased familia incidence in the form of a single mendelian dominance is also noted in the pediatric age groups. We report an 11 years old girl who presented with paroxysmal hypertension and an extra-adrenal, midline pheochromocytomia in the region of the celiac axis. To our knowledge, this specific location has been reported in the literature only once. Diagnostic and therapheutic problemas arose as a consequence of its uncommon presentation and anatomic location