Extrahepatic portal hypertension due to familial protein S deficiency.
Indian Pediatr
;
2009 Jan; 46(1): 70-1
Artículo
en Inglés
| IMSEAR
| ID: sea-12211
ABSTRACT
Portal vein thrombosis (PVT) is a common cause of portal hypertension in children. A majority of children with PVT of unknown etiology have functional Protein C deficiency or abnormally elevated levels of anti-cardiolipin antibodies. We report an 8 years old Indian girl with portal cavernoma due to hereditary Protein S deficiency. We documented familial deficiency of Protein S in 2 asymptomatic siblings suggesting that this deficiency is the primary cause of portal vein thrombosis.
Texto completo:
Disponible
Índice:
IMSEAR (Asia Sudoriental)
Asunto principal:
Vena Porta
/
Femenino
/
Humanos
/
Niño
/
Deficiencia de Proteína S
/
Trombosis de la Vena
/
Hipertensión Portal
Idioma:
Inglés
Revista:
Indian Pediatr
Año:
2009
Tipo del documento:
Artículo
Similares
MEDLINE
...
LILACS
LIS