Shone's Anomaly - A Case Report.

ABSTRACT

Shone's anomaly, a rare congenital cardiac malformation consists of multiple levels of left heart obstruction - supravalvar mitral ring, parachute mitral value, subaortic stenosis and coarctation of the aorta. Although they present with a wide spectrum of major anatomical and haemodynamic abnormalities, a satisfactory outcome is possible for most patients. The operative mortality and outcome is affected by the severity of mitral value disease and the need for multiple operative procedures. We report one such case with this anomaly who presented to us in the third decade. He underwent a two - stage procedure in a single sitting successfully.