De Novos Presentation of Cannon’s Disease.

ABSTRACT

White spongy nevus (WSN) is a rare hereditary disorder belonging to genodermatosis with a suggested etiology as a mutation in a gene.1 Lesions usually appear in younger age which can be seen in any part of the oral mucosa.2 WSN can affect any mucosa in body with or without oral involvement. A 12-year-old female patient came to our department for dental evaluation. A general examination of body showed no abnormalities. The intraoral examination revealed generalized white patches in the oral mucosa with the wrinkled surface (Figures 1-4). The lesion was totally asymptomatic and the patient was aware of roughness in oral mucosa which she noticed from her childhood. There were no mucosal changes anywhere in the body. There was no history of a similar lesion in family members. An incisional biopsy was done from the buccal mucosa. Fromclinical and histopathological features, we arrived at a diagnosis of WSN.