Isolated ileal ganglioneuromatosis in an 11‑year‑old boy: Case report and review of literature.
Indian J Pathol Microbiol
;
2016 July-Sept 59(3): 365-367
Artículo
en Inglés
| IMSEAR
| ID: sea-179581
ABSTRACT
Ganglioneuromatous proliferation in the gastrointestinal tract is a rare occurrence and is usually associated with specific syndrome complexes such as multiple endocrine neoplasia Type 2B or von Recklinghausen’s disease. We report here a case of diffuse intestinal ganglioneuromatosis, presenting as intestinal obstruction and chronic constipation in an 11‑year‑old boy. Sporadic cases of intestinal ganglioneuromatosis in the absence of any systemic manifestations are a very rare cause of enteric motility disorders in childhood, and we discuss the pathological and clinical significance of this finding. Histopathological identification of this uncommon cause of a common pediatric problem is important since the condition is amenable to surgical treatment.
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IMSEAR (Asia Sudoriental)
Tipo de estudio:
Estudio pronóstico
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Inglés
Revista:
Indian J Pathol Microbiol
Año:
2016
Tipo del documento:
Artículo
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