Severe Bladder Outlet Obstruction in a 7-Week-Old Infant Presenting with Features of Prune Belly Syndrome: A Case Report

ABSTRACT

Prune Belly syndrome is characterized by urinary tract anomalies, deficient abdominal muscle and bilateral cryptorchidism. It has an incidence of about 1 in 50,000 live births with male preponderance in 95%. This is a 7 weeks old male infant that was referred from a peripheral health care centre for a micturating cystourethrography on account of difficulty in micturition, distended abdomen and restlessness since birth. The patient had an abdominal ultrasonography that showed bilateral severe hydronephrosis, megaureters and thick-walled urinary bladder. A micturating cystourethrogram showed pine shaped urinary bladder with bilateral vesicoureteric reflux more marked on the right. Plain abdominal radiograph showed markedly distended abdomen and gas distended bowel loops with thinning of anterior abdominal wall muscles. The referring physician was advised to make a prompt referral of this case to a higher centre for better management. We report the radiologic findings of this case presenting with features of Prune Belly syndrome.