Hereditary angioedema caused by C1-esterase inhibitor deficiency: a case report with literature-based analysis
Artículo
| IMSEAR
| ID: sea-206480
ABSTRACT
Hereditary angioedema (HAE) caused by C1-esterase inhibitor deficiency is an autosomal-dominant disease caused by a mutation in the C1-inhibitor gene. It is a rare disease that is often worsened during pregnancy and childbirth. HAE, though uncommon but if untreated it may lead to maternal death. The case report presents the successful management of a 24 years old, G2P1, with hereditary angioedema caused by C1-esterase inhibitor deficiency. This patient was managed with a multidisciplinary approach by an obstetrician, an immunologist, an anaesthesiologist and a pediatrician. She had an uneventful antenatal period, labor was induced. She had precipitate delivery and soon after delivery had a flare up of the disease. It was successfully managed with fresh frozen plasma and close observation.
Texto completo:
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Índice:
IMSEAR (Asia Sudoriental)
Año:
2019
Tipo del documento:
Artículo
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