Papillon-Lefevre syndrome: two case reports.
Artículo
en Inglés
| IMSEAR
| ID: sea-51876
ABSTRACT
Papillon-Lefevre syndrome is a rare autosomal recessive disorder in which there is palmoplantar keratinization and premature loss of both deciduous and permanent teeth. The palmoplantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at the age of 3 or 4 years. An early diagnosis of the syndrome can help preserve the teeth by early institution of treatment, using a multidisciplinary approach. We present two cases of the syndrome having all of the characteristic features.
Texto completo:
Disponible
Índice:
IMSEAR (Asia Sudoriental)
Asunto principal:
Enfermedad de Papillon-Lefevre
/
Periodontitis
/
Exfoliación Dental
/
Femenino
/
Humanos
/
Masculino
/
Pérdida de Hueso Alveolar
/
Adolescente
/
Gingivitis
Tipo de estudio:
Estudio de tamizaje
Idioma:
Inglés
Año:
2007
Tipo del documento:
Artículo
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