A case of erythropoietic protoporphyria / 대한피부과학회지
Korean Journal of Dermatology
;
: 817-822, 1993.
Artículo
en Coreano
| WPRIM
| ID: wpr-101006
ABSTRACT
Erythropoietic protoporphyria, sometimes also called erythrohepitic protoporphyria or simple protoporphyria, is a heritable detect of heme synthesis in which the last enzyme of the heme synthetic pathway, ferrochelatase(or heme synthetase), is functioning subopt,imally. A 23-year-old male has experi nced erythema and edema on the fae and hands during or immediately after sun exposure, since 3 years of age. The skin lesions have been accompanied by severe itching, a buring sensation and pain. Severe episodes were followed hy head iche and vomiting. We have seen a case of erythropoietic protoporphyria presenting clinically and histo athologically, wit.h a skin lesion on the sun exposured area, and free erthrocyte protoporphyrin serologically.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Prurito
/
Sensación
/
Piel
/
Vómitos
/
Sistema Solar
/
Protoporfiria Eritropoyética
/
Edema
/
Eritema
/
Mano
/
Cabeza
Límite:
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Korean Journal of Dermatology
Año:
1993
Tipo del documento:
Artículo
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