Spontaneously Regressed Immunoglobulin IgG4-related Lung Disease Presenting as Multiple Cavitary Nodules / 대한내과학회지
Korean Journal of Medicine
; : 449-454, 2016.
Article
en Ko
| WPRIM
| ID: wpr-101315
Biblioteca responsable:
WPRO
ABSTRACT
Immunoglobulin (Ig) G4-related disease was recently recognized as a systemic fibro-inflammatory disease characterized by dense lymphoplasmacytic infiltrates, storiform fibrosis, and obliterative phlebitis with IgG4-positive cells in the target tissues. This disease can localize to a single organ or be diffuse in multiple organs. Pulmonary manifestation in IgG4-related lung disease presents as various sized nodules, lung masses, patchy ground-glass opacities, consolidation, thickened bronchovascular bundles, nodular pleural lesions, and interstitial lung disease. Traditional treatment for IgG4-related lung disease includes systemic (cortico) steroids. Here, we report a case of IgG4-related lung disease presenting as multiple cavitary nodules that spontaneously regressed without systemic steroid use.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Flebitis
/
Esteroides
/
Fibrosis
/
Inmunoglobulina G
/
Inmunoglobulinas
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Corticoesteroides
/
Enfermedades Pulmonares Intersticiales
/
Nódulos Pulmonares Múltiples
/
Pulmón
/
Enfermedades Pulmonares
Idioma:
Ko
Revista:
Korean Journal of Medicine
Año:
2016
Tipo del documento:
Article