A Case of IgG4-Related Lung Disease Mimicking Non-Specific Interstitial Pneumonia / 대한내과학회지
Korean Journal of Medicine
;
: 308-312, 2015.
Artículo
en Coreano
| WPRIM
| ID: wpr-103789
ABSTRACT
Immunoglobulin (Ig) G4-related disease is a recently described systemic inflammatory disease characterized by high serum IgG4 concentrations and sclerosing inflammation of numerous IgG4-positive plasma cells that responds favorably to steroid treatment. Although initial description of this disorder focused on its pancreatic presentation, it has become apparent that it is a systemic disease. In this report, we describe a case of IgG4-related lung disease presenting as non-specific interstitial pneumonia in a 78-year-old male with interstitial lung disease. Pathological examination through video-assisted thoracic surgery showed a non-specific interstitial pneumonia pattern and numerous (> 50/high-power field) infiltrating IgG4-positive plasma cells. Laboratory tests also revealed a high serum IgG4 concentration. Prednisolone therapy was initiated and his symptoms and reticular opacity improved after two months of treatment.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Células Plasmáticas
/
Inmunoglobulina G
/
Inmunoglobulinas
/
Prednisolona
/
Enfermedades Pulmonares Intersticiales
/
Cirugía Torácica Asistida por Video
/
Inflamación
/
Enfermedades Pulmonares
Límite:
Anciano
/
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Korean Journal of Medicine
Año:
2015
Tipo del documento:
Artículo
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