A Case of Lymphangioleiomyomatosis in Lung / 영남의대학술지
Yeungnam University Journal of Medicine
;
: 63-68, 2010.
Artículo
en Coreano
| WPRIM
| ID: wpr-106381
ABSTRACT
Lymphangioleiomyomatosis (LAM) is a rare, cystic lung disease that is associated with mutation in the tuberous sclerosis genes, renal angiomyolipomas, lymphatic spread and a remarkable female gender predilection. The pathology of LAM is represented by the proliferation of immature smooth muscle cells in the walls of airways, and venules and lymphatic vessels in the lung. The clinical course of LAM is characterized by progressive dyspnea on exertion, recurrent pneumothorax and collections of chylous fluid. The diagnosis of pulmonary LAM can be made on chest X-ray, a high-resolution CT scan and lung biopsy. We experienced a case of pulmonary lymphangioleiomyomatosis in a 28-years-old female patient who had suffered from progressive dyspnea on exertion, so we report on it along with a brief review of the relevant literature.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Neumotórax
/
Tórax
/
Esclerosis Tuberosa
/
Vénulas
/
Biopsia
/
Lipopolisacáridos
/
Linfangioleiomiomatosis
/
Angiomiolipoma
/
Miocitos del Músculo Liso
/
Vasos Linfáticos
Límite:
Femenino
/
Humanos
Idioma:
Coreano
Revista:
Yeungnam University Journal of Medicine
Año:
2010
Tipo del documento:
Artículo
Similares
MEDLINE
...
LILACS
LIS