Febrile Ulceronecotic Pityriasis Lichenoides et Varioliformis Acuta Successfully Treated with Oral Cyclosporin / 대한피부과학회지
Korean Journal of Dermatology
;
: 565-568, 2012.
Artículo
en Inglés
| WPRIM
| ID: wpr-106450
ABSTRACT
Febrile ulceronecrotic pityriasis lichenoides et varioliformis acuta (PLEVA), or febrile ulcerative Mucha-Haberman disease (FUMHD) is very rare, but potentially lethal variants of PLEVA. This subtype is characterized by rapidly progressive ulceronecrotic lesions and systemic manifestations, such as high fever, gastrointestinal, neurological, cardiologic and pulmonary involvement, and rheumatologic manifestations. Several treatments with variable response have been challenged, such as systemic steroid, antibiotics, methotrexate, dapsone, cyclosporine and ultraviolet therapy. But there is no standard therapy for FUMHD to date. We report a 59-year-old woman with FUMHD, who recurred after discontinuation of systemic steroid, but successfully treated with oral cyclosporine.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Pitiriasis
/
Úlcera
/
Terapia Ultravioleta
/
Metotrexato
/
Ciclosporina
/
Pitiriasis Liquenoide
/
Dapsona
/
Fiebre
/
Antibacterianos
Límite:
Femenino
/
Humanos
Idioma:
Inglés
Revista:
Korean Journal of Dermatology
Año:
2012
Tipo del documento:
Artículo
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