A Case of Repeated Ventricular Tachycardia Caused by Cardiac Rhabdomyomas in an Infant with Tuberous Sclerosis
Journal of the Korean Pediatric Society
;
: 913-917, 2003.
Artículo
en Coreano
| WPRIM
| ID: wpr-112016
ABSTRACT
Cardiac rhabdomyomas are relatively uncommon and associated with tuberous sclerosis in 40-50% cases. We report a 10-month-old infant with tuberous sclerosis who presented with ventricular arrythmias and status epilepticus. There were hypopigmented macules on the body, periventricular calcifications, renal cyst and cardiac rabdomyomas just below the aortic valve. The patient required resection of left ventricular subaortic masses due to sustained arrythmia in spite of intravenous amiodarone therapy. The pathologic examination confirmed the diagnosis of rhabdomyoma. The patient had no more arrythmia during the 14 month follow up period. Although cardiac rhabdomyomas may spontaneously regress, surgery is often necessary and frequently resolves the underlying arrythmia.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Válvula Aórtica
/
Arritmias Cardíacas
/
Rabdomioma
/
Estado Epiléptico
/
Esclerosis Tuberosa
/
Estudios de Seguimiento
/
Taquicardia Ventricular
/
Diagnóstico
/
Amiodarona
Tipo de estudio:
Estudio diagnóstico
/
Estudio observacional
/
Estudio pronóstico
Límite:
Humanos
/
Lactante
Idioma:
Coreano
Revista:
Journal of the Korean Pediatric Society
Año:
2003
Tipo del documento:
Artículo
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