Bronchoscopic concerns in Proteus syndrome: a case report / 대한마취과학회지
Korean Journal of Anesthesiology
; : 523-526, 2016.
Article
en En
| WPRIM
| ID: wpr-123002
Biblioteca responsable:
WPRO
ABSTRACT
Proteus syndrome (PS) is a rare congenital hamartomatous disorder with multisystem involvement. PS shows highly clinical variability due to overgrowth of the affected areas, and several features can make anesthetic management challenging. Little is known about the airway problem associated with anesthesia in PS patients. An 11-year-old girl with PS was scheduled for ear surgery under general anesthesia. She had features complicating intubation including facial asymmetry and disproportion, abnormal teeth, limitation of neck movement due to torticollis, and thoracolumbar scoliosis. This study reports on a case of deformed airway of a PS patient under fiberoptic bronchoscopy.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Proteus
/
Escoliosis
/
Diente
/
Tortícolis
/
Broncoscopía
/
Síndrome de Proteo
/
Oído
/
Asimetría Facial
/
Intubación
/
Anestesia
Límite:
Child
/
Female
/
Humans
Idioma:
En
Revista:
Korean Journal of Anesthesiology
Año:
2016
Tipo del documento:
Article