A Case of Congenital Disseminated Malignant Rhabdoid Tumor of the Soft Tissue in Neonate / 대한주산의학회잡지
Korean Journal of Perinatology
; : 311-316, 2010.
Article
en Ko
| WPRIM
| ID: wpr-130993
Biblioteca responsable:
WPRO
ABSTRACT
Malignant rhabdoid tumor (MRT) was first described as a "rhabdomyosarcomatoid" variant of Wilms tumor, but was later identified as a distinct entity. MRTs are extremely rare and highly aggressive neoplasm with poor outcome, occurring mostly in kidneys and central nervous system, less frequently in extrarenal sites. MRTs are referred to as "congenital" when it is diagnosed at or immediately after birth. There are few reports about congenital disseminated MRT at birth. We report a case of congenital malignant rhabdoid tumor presenting as a soft tissue mass in the right arm at birth although the autopsy revealed the systemic disseminated tumors through the whole body with typical microscopic findings.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Brazo
/
Autopsia
/
Sistema Nervioso Central
/
Tumor Rabdoide
/
Tumor de Wilms
/
Parto
/
Riñón
Tipo de estudio:
Prognostic_studies
Límite:
Humans
/
Newborn
Idioma:
Ko
Revista:
Korean Journal of Perinatology
Año:
2010
Tipo del documento:
Article