Otologic Manifestation in IgG4-Related Systemic Disease
Clinical and Experimental Otorhinolaryngology
; : 52-54, 2011.
Article
en En
| WPRIM
| ID: wpr-133446
Biblioteca responsable:
WPRO
ABSTRACT
IgG4-related systemic disease, including autoimmune pancreatitis, is a multi-organ disorder characterized by elevated serum immunoglobulin G4 (IgG4) concentration and IgG4-positive plasma cell infiltration. We report a case of a 66-year-old woman with IgG4-related hearing disorder, presenting with fluctuating mixed hearing loss with middle ear effusion. The serum IgG4 level was elevated and pathological examination revealed dense infiltration of IgG4-positive lymphocyte in the renal parenchyma, lung tissue and lacrimal gland. With intravenous methylprednisolone at a dose of 60 mg daily, improvement of hearing loss were observed. No recurrence was observed for 6 months with mainternance of prednisolone and methotrexate.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Pancreatitis
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Células Plasmáticas
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Recurrencia
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Enfermedades Autoinmunes
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Otitis Media con Derrame
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Inmunoglobulina G
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Inmunoglobulinas
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Metilprednisolona
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Prednisolona
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Linfocitos
Límite:
Aged
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Female
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Humans
Idioma:
En
Revista:
Clinical and Experimental Otorhinolaryngology
Año:
2011
Tipo del documento:
Article