IgG4-Related Systemic Disease Can Be Easily Mistaken as a Uroepithelial Tumor / 전남의대학술지
Chonnam Medical Journal
; : 39-42, 2015.
Article
en En
| WPRIM
| ID: wpr-133646
Biblioteca responsable:
WPRO
ABSTRACT
Immunoglobulin G4-related disease (IgG4-RD) is a newly recognized systemic syndrome characterized by elevated serum IgG4 concentrations and tumefaction or tissue infiltration by IgG4-positive plasma cells. We experienced a case of IgG4-RD involving multiple organs in a 64-year-old female who was referred for a suspected uroepithelial tumor. A mass biopsy confirmed dense lymphoplasmacytic infiltration with an increased number of IgG4-positive plasma cells. We discuss this case and review the literature to bring IgG4-RD to the attention to clinicians because it responds dramatically well to steroid therapy and should be kept in mind as a differential diagnosis to avoid unnecessary surgery.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Células Plasmáticas
/
Esclerosis
/
Biopsia
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Inmunoglobulina G
/
Inmunoglobulinas
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Procedimientos Innecesarios
/
Diagnóstico Diferencial
/
Riñón
Tipo de estudio:
Diagnostic_studies
Límite:
Female
/
Humans
Idioma:
En
Revista:
Chonnam Medical Journal
Año:
2015
Tipo del documento:
Article