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Weber-Christian disease presenting with proptosis: a case report
Journal of Korean Medical Science ; : 247-250, 2000.
Artículo en Inglés | WPRIM | ID: wpr-140416
ABSTRACT
Weber-Christian disease (WCD) is a rare inflammatory disease of adipose tissue, which is characterized by painful cutaneous nodules and constitutional symptoms. Although any area of the body containing fat can be affected by WCD, the involvement of retrobulbar fat is uncommon and proptosis is a rare presenting manifestation. We report a case who presented with proptosis of the right eye which is accompanied by painful subcutaneous nodules, high fever and myalgia. Biopsies of retrobulbar tissue and suprapubic nodule showed lobular panniculitis with mixed cellular infiltration, mainly composed of histiocytes and lymphocytes. He responded well to high-dose glucocorticoid.
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Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Biopsia / Imagen por Resonancia Magnética / Paniculitis Nodular no Supurativa / Exoftalmia / Glucocorticoides Límite: Adulto / Humanos / Masculino Idioma: Inglés Revista: Journal of Korean Medical Science Año: 2000 Tipo del documento: Artículo

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Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Biopsia / Imagen por Resonancia Magnética / Paniculitis Nodular no Supurativa / Exoftalmia / Glucocorticoides Límite: Adulto / Humanos / Masculino Idioma: Inglés Revista: Journal of Korean Medical Science Año: 2000 Tipo del documento: Artículo