A Case of Superior Mesenteric Artery Aneurysm associated with Marfan Syndrome

ABSTRACT

Superior mesenteric artery aneurysm is very rare complication of Marfan syndrome, especially in children. A 11 years old male patient was admitted to the hospital because of fluctuating high fever and diagnosed as infective endocarditis and Marfan syndrome. During antibiotics therapy, fever was slowly decreased but abdominal pain was developed and pulsatile abdominal mass was palpable in the midline of the abdomen. And the diagnosis was made as superior mesenteric artery aneurysm by ultrasonogaphy and abdominal aortogram. Resection of aneurysm was performed successfully. A brief review of the related literatures was made.