A Case of Male Pseudohermaphroditism due to 17alpha-Hydroxylase Deficiency / 대한불임학회지
Korean Journal of Fertility and Sterility
;
: 133-138, 2006.
Artículo
en Coreano
| WPRIM
| ID: wpr-151306
ABSTRACT
Female phenotype of a 46,XY male may originates from male pseudohermaphroditism due to 17alpha-hydroxylase deficiency. Lack of cortisol increases adrenocorticotropic hormone (ACTH) and mineralocorticoid production, leading to low renin hypertention and hypokalemia. A 41-year-old phenotypic female presented primary amenorrhea and hypertension. In the hormonal profile, the levels of serum estradiol, testosterone, rennin, and cortisol were decreased and ACTH and deoxycorticosterone were increased. Laparoscopic bilateral gonadectomy was performed, and corticosteroid, antihypertensive drugs, and estrogen were administered. We report this case with a brief review of the literatures.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Fenotipo
/
Testosterona
/
Hidrocortisona
/
Quimosina
/
Renina
/
Hiperplasia Suprarrenal Congénita
/
Hormona Adrenocorticotrópica
/
Desoxicorticosterona
/
Estradiol
/
Estrógenos
Límite:
Adulto
/
Femenino
/
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Korean Journal of Fertility and Sterility
Año:
2006
Tipo del documento:
Artículo
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