Congenital Absence of the Portal Vein in an Adult Man Presenting with Portosystemic Encephalopathy: A Case Report

ABSTRACT

Congenital absence of the portal vein is a rare anomaly in which diverse types of congenital portosystemic shunts are present. In this report, we describe this rare anomaly of a portosystemic shunt between the inferior mesenteric vein and left internal iliac vein, in a middle-aged man presenting with portosystemic encephalopathy.