A Case of Hepatoblatoma with Intraatrial Extension / 대한소아혈액종양학회지

ABSTRACT

Hepatoblastoma is an uncommon malignant tumor of the liver in children, moreover its intracaval extension to the right atrium is extremely rare. Current data indicate that combined hepatectomy and resection of intraatrial extension is necessary for cure. However 40% of the patients present with tumor that would make primary complete resection impossible or extremely hazardous. In these case preoperative chemotherapy is recommanded. We recently experienced a rare case of hepatoblastoma which metastasized to lung and to right atrium via inferior vena cava. We report this case with brief review of literature.