A case of idiopathic pulmonary hemosiderosis with seasonal recurrence / 소아과
Korean Journal of Pediatrics
; : 256-260, 2009.
Article
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| WPRIM
| ID: wpr-157905
Biblioteca responsable:
WPRO
ABSTRACT
Idiopathic pulmonary hemosiderosis (IPH) is a rare disease affecting mostly children. This disorder is characterized by recurrent episodes of hemoptysis, bilateral diffuse pulmonary infiltrates, and iron-deficiency anemia. An acute fulminant alveolar hemorrhage can be fatal due to respiratory failure, while chronic hemorrhage leads to hemosiderin-laden macrophages and pulmonary fibrosis. Genetic, autoimmune, allergic, environmental, and metabolic mechanisms of pathogenesis have been suggested, but the etiology of IPH remains unknown. We report on a 9-year-old girl with idiopathic pulmonary hemosiderosis who showed seasonal recurrences without cause.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Fibrosis Pulmonar
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Recurrencia
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Insuficiencia Respiratoria
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Estaciones del Año
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Anemia Ferropénica
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Enfermedades Raras
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Hemoptisis
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Hemorragia
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Hemosiderosis
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Enfermedades Pulmonares
Límite:
Child
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Humans
Idioma:
En
Revista:
Korean Journal of Pediatrics
Año:
2009
Tipo del documento:
Article