Necrobiotic Xanthogranuloma with Monoclonal Gammopathy / 대한피부과학회지
Korean Journal of Dermatology
; : 152-155, 2012.
Article
en Ko
| WPRIM
| ID: wpr-165115
Biblioteca responsable:
WPRO
ABSTRACT
Necrobiotic xanthogranuloma (NXG) is a rare, progressive, histiocytic disease characterized by destructive cutaneous lesions, a close association with paraproteinemia, multiple myeloma, hypertension, and multiple extracutaneous manifestations. Multiple indurated yellow-red plaques or nodules are commonly present in this disorder. The pathogenesis of NXG is poorly understood. Histopathologically, NXG features with hyaline necrosis or necrobiosis are present. We describe a patient with typical cutaneous and histologic findings of NXG with an associated monoclonal gammopathy.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Paraproteinemias
/
Trastornos Necrobióticos
/
Xantogranuloma Necrobiótico
/
Hialina
/
Hipertensión
/
Mieloma Múltiple
/
Necrosis
Límite:
Humans
Idioma:
Ko
Revista:
Korean Journal of Dermatology
Año:
2012
Tipo del documento:
Article