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A Case of Epidermolytic Keratosis Palmaris et Plantaris / 대한피부과학회지
Korean Journal of Dermatology ; : 678-681, 1985.
Artículo en Coreano | WPRIM | ID: wpr-178181
ABSTRACT
Epidermolytic keratosis palmaris is a rare disease which shows clinical findings of Unna Thost keratoderma and histopathologic of epidermolytic hyperkeratosis. We report herein a case of epidermolytic keratosis palmaris et plantaris in a 16-month-old female baby. Light microscopy shows marked hyperkeratosis, large irregular keratohyalin granules, and large clear spaces in the granular and upper spinous layers. Eletron microscopic findings shows that the clear spaces are areas of cytoplasm filled with a fibrillar material and cellular organelles. Abnormal clumping of tonofilament and keratohyalin is also present.
Asunto(s)

Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Filamentos Intermedios / Orgánulos / Hiperqueratosis Epidermolítica / Queratodermia Palmoplantar / Citoplasma / Enfermedades Raras / Queratosis / Microscopía Límite: Femenino / Humanos / Lactante Idioma: Coreano Revista: Korean Journal of Dermatology Año: 1985 Tipo del documento: Artículo

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Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Filamentos Intermedios / Orgánulos / Hiperqueratosis Epidermolítica / Queratodermia Palmoplantar / Citoplasma / Enfermedades Raras / Queratosis / Microscopía Límite: Femenino / Humanos / Lactante Idioma: Coreano Revista: Korean Journal of Dermatology Año: 1985 Tipo del documento: Artículo