Localized Fibrosing Mediastinitis with Superior Vena Caval(SVC) Syndrome / 결핵및호흡기질환
Tuberculosis and Respiratory Diseases
;
: 387-391, 2007.
Artículo
en Coreano
| WPRIM
| ID: wpr-179425
ABSTRACT
Fibrosing mediastinitis is a rare disease that is characterized by the proliferation of dense fibrous tissue of the mediastinum. The pathogenesis of fibrosing mediastinitis is unknown in most cases. However, histoplasmosis, tuberculosis, autoimmune disease, radiation therapy, and other idiopathic fibroinflammatory diseases have been implicated in some cases. Most clinical features are related to an obstruction or compression of the mediastinal structure. Fibrosing mediastinitis is often progressive and occurs diffusely throughout the mediastinum. We encountered a case of fibrosing mediastinitis of a very focal lesion without evidence of mediastinal involvement. The condition was confirmed by biopsy and graft bypass surgery was performed because of SVC syndrome.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Enfermedades Autoinmunes
/
Tuberculosis
/
Biopsia
/
Trasplantes
/
Enfermedades Raras
/
Histoplasmosis
/
Mediastinitis
/
Mediastino
Idioma:
Coreano
Revista:
Tuberculosis and Respiratory Diseases
Año:
2007
Tipo del documento:
Artículo
Similares
MEDLINE
...
LILACS
LIS