IgG4-Related Sclerosing Cholangitis Showing Natural Course of Progression to Decompensated Liver Cirrhosis / 대한췌담도학회지
Korean Journal of Pancreas and Biliary Tract
;
: 179-183, 2017.
Artículo
en Coreano
| WPRIM
| ID: wpr-180596
ABSTRACT
Immunoglobulin G4-related disease (IgG4-RD) is characterized by extensive IgG4-positive plasma cells infiltration resulting in inflammation and fibrosis of the affected organs. Patient with IgG4-RD shows an excellent response to glucocorticoid therapy especially when given at early onset stages. IgG4-related sclerosing cholangitis (IgG4-SC) is considered biliary manifestation of IgG4-RD. The natural history and long-term prognosis of IgG4-SC is not well defined and most of the previous case series have reported short duration of follow-up. We present the case of development of decompensated liver cirrhosis from IgG4-related sclerosing cholangitis with a 6-year natural clinical course.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Células Plasmáticas
/
Pronóstico
/
Fibrosis
/
Inmunoglobulinas
/
Colangitis Esclerosante
/
Colangitis
/
Estudios de Seguimiento
/
Historia Natural
/
Inflamación
/
Hígado
Tipo de estudio:
Estudio observacional
/
Estudio pronóstico
Límite:
Humanos
Idioma:
Coreano
Revista:
Korean Journal of Pancreas and Biliary Tract
Año:
2017
Tipo del documento:
Artículo
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