An anesthetic experience in a patient with Stickler sydrome: A case report
Anesthesia and Pain Medicine
;
: 85-88, 2011.
Artículo
en Coreano
| WPRIM
| ID: wpr-192485
ABSTRACT
Stickler syndrome is a connective tissue dysplasia disorder with characteristic midface hypoplasia, retromicrognathia, cleft palate, and a moon-shaped appearance. Incidence of the syndrome is estimated at around 1/10000 and the disorder is considered to be caused by mutations in the COL2A1, COL11A1, COL11A2, COL9A1 procollagen genes of type 2 and 11 collagen. Patients with a mandibular hypoplasia like Stickler syndrome present the anesthesiologist with considerable problems when mask ventilation or endotracheal intubation is attempted. We report a successful anesthetic experience, including blind endotracheal intubation with rigid laryngoscope without neuromuscular blockade, in a 9-year-old boy with Stickler syndrome for scleral buckling with cryotherapy.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Curvatura de la Esclerótica
/
Ventilación
/
Incidencia
/
Colágeno
/
Fisura del Paladar
/
Procolágeno
/
Crioterapia
/
Tejido Conectivo
/
Bloqueo Neuromuscular
/
Laringoscopios
Tipo de estudio:
Estudio de incidencia
/
Estudio pronóstico
Límite:
Niño
/
Humanos
Idioma:
Coreano
Revista:
Anesthesia and Pain Medicine
Año:
2011
Tipo del documento:
Artículo
Similares
MEDLINE
...
LILACS
LIS