Pyridoxine responsive sideroblastic anemia in a boy with mitral valve prolapse / 소아과
Korean Journal of Pediatrics
; : 1223-1226, 2006.
Article
en En
| WPRIM
| ID: wpr-19354
Biblioteca responsable:
WPRO
ABSTRACT
Sideroblastic anemia is a rare, heterogeneous group of disorders characterized by hyperferremia, microcytic hypochromic anemia, and bone marrow erythroid hyperplasia with the presence of numerous ringed sideroblasts. We describe herewith the case of a rare coincidence of sideroblastic anemia and mitral valve prolapse with resultant regurgitation in a 2-year-old boy. In addition to the inherent propensity for the development of cardiac dysfunction in sideroblastic anemia due to transfusion-associated myocardial iron overload and chronic anemia, a coincidence of MVP will further increase the likelihood of the morbidity or mortality of th patient. in this patient. After response to pyridoxine, the patient remains in good condition with stable hemoglobin levels.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Piridoxina
/
Médula Ósea
/
Mortalidad
/
Prolapso de la Válvula Mitral
/
Sobrecarga de Hierro
/
Hiperplasia
/
Anemia
/
Anemia Hipocrómica
/
Anemia Sideroblástica
/
Válvula Mitral
Tipo de estudio:
Prognostic_studies
Límite:
Child, preschool
/
Humans
/
Male
Idioma:
En
Revista:
Korean Journal of Pediatrics
Año:
2006
Tipo del documento:
Article