Surgical Treatment of Choanal Stenosis Associated with Craniodiaphyseal Dysplasia
Journal of the Korean Cleft Palate-Craniofacial Association
; : 61-64, 2004.
Article
en Ko
| WPRIM
| ID: wpr-193882
Biblioteca responsable:
WPRO
ABSTRACT
Craniodiaphyseal dysplasia is a rare genetic disorder of bone due to modelling errors of long bones and skull bones. Facial and cranial thickening and distortion are particularly striking in this form. The genetic understanding of this disorder is unsatisfactory. We present one case of Craniodiaphyseal dysplasia involving facial bone, skull that causes nasal obstruction. This 3-year old female who was diagnosed of craniodiaphyseal dysplasia presented abnormal facial figuring, which is excessively thickened cortical bone resulting in very large craniofacial bony structure. The patient sufferred from respiratory difficulty due to complete obstruction of choana. We performed surgical recanalization of choanal atresia by transpalatal approach and gained good postoperative result.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Cráneo
/
Huelga de Empleados
/
Obstrucción Nasal
/
Atresia de las Coanas
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Constricción Patológica
/
Huesos Faciales
Límite:
Child, preschool
/
Female
/
Humans
Idioma:
Ko
Revista:
Journal of the Korean Cleft Palate-Craniofacial Association
Año:
2004
Tipo del documento:
Article