Intrathoracic malignant peripheral nerve sheath tumor in von Recklinghausen's disease
The Korean Journal of Internal Medicine
;
: 201-204, 2001.
Artículo
en Inglés
| WPRIM
| ID: wpr-194509
ABSTRACT
Malignant peripheral nerve sheath tumor (MPNST) is defined as any malignant tumor arising from or differentiating toward the cells of the peripheral nerve sheath. MPNST accounts for about 5-10% of all soft tissue tumors and is often associated with neurofibromatosis type I (NF-1, von Recklinghausen's disease). It is one of the malignant tumors associated with von Recklinghausen's disease. Its common site is the lower and upper extremities, trunk, head and neck. But intrathoracic manifestations are very rare. We report a case of a 40 year-old man with multiple neurofibromatosis who was presented with an intrathoracic malignant peripheral nerve sheath tumor
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Pronóstico
/
Neoplasias Torácicas
/
Índice de Severidad de la Enfermedad
/
Diafragma
/
Neurofibromatosis 1
/
Neoplasias de la Vaina del Nervio
/
Pulmón
Tipo de estudio:
Estudio pronóstico
Límite:
Adulto
/
Humanos
/
Masculino
Idioma:
Inglés
Revista:
The Korean Journal of Internal Medicine
Año:
2001
Tipo del documento:
Artículo
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