Surgical Outcome of Familial Lens Dislocation in Two Families

ABSTRACT

The congenital lens dislocation is a uncommon genetic disease, which is inherited autosomal dominant mannner and less likely autosomal recessive. The cause of the disease has not been fully understood although there are some hypothesis based on developmental anomaly. There are controversies about the management of the disease. In these days, early surgery is usually performed to prevent the compilcation. The authors experienced five patients in two families and three of them were operated with good results. They showed autosomal dominaot inheritance pattern. So, we present five cases of uncommon congenital lens dislocation with a brief review of literature.