Morbihan Disease: A Rare Variant of Rosacea / 대한피부과학회지
Korean Journal of Dermatology
;
: 320-323, 2012.
Artículo
en Coreano
| WPRIM
| ID: wpr-215287
ABSTRACT
Morbihan disease, also known as 'rosacea lymphedema' or 'solid persistent facial edema' was first reported by Degos, in 1957, for describing persistent lymphedema on the upper half of the face in association with rosacea. Although the pathogenesis of Morbihan disease is not established well, two hypotheses were proposed; firstly, the hypothesis of lymphatic obstruction by destruction of vessel supporting connective tissue (e.g. elastin), and secondly, the hypothesis of mast cell-induced fibrosis. Herein, we report a 71-year-old man who had 9-months history of persistent bilateral edema of the eyelids. The histopathologic exam from edematous eyelid revealed marked dermal edema, dilated vascular structure with perivascular mixed cellular inflammatory infiltration. Moreover, focal granulomatous infiltration adjacent to a vascular structure and numerous mast cells were also identified. This case is the first reported case of Morbihan disease in Korean dermatological literature. Furthermore, the histopathologic findings of this case support both of the two hypotheses for development of Morbihan disease.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Fibrosis
/
Rosácea
/
Tejido Conectivo
/
Edema
/
Párpados
/
Glicosaminoglicanos
/
Linfedema
/
Mastocitos
Tipo de estudio:
Estudio pronóstico
Límite:
Anciano
/
Humanos
Idioma:
Coreano
Revista:
Korean Journal of Dermatology
Año:
2012
Tipo del documento:
Artículo
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