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A Case of Hypertrophic Cardiomyopathy Associated with Wolff-Parkinson-White Syndrome
Journal of the Korean Pediatric Cardiology Society ; : 181-186, 2004.
Artículo en Coreano | WPRIM | ID: wpr-218442
ABSTRACT
Hypertrophic cardiomyopathy(HCM) is defined as a thickened wall of heart muscles and non-dilated left ventricle, but is not accompanied underlying cardiac or systemic diseases that induce ventricular hypertrophy. HCM is responsible to exercise limitation for all ages and also is known as the most common cause of heart-related sudden death during childhood and adolescents. Epidemiological studies showed that prevalence in young adults is 0.2% and HCM is caused by a mutations in genes that code the proteins of cardiac muscles. HCM with Wolff-Parkinson-White Syndrome is extremely rare and associated with a high risk of tachyarrhythmia and sudden death. We report an infantile HCM with WPW syndrome who died suddenly.
Asunto(s)

Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Taquicardia / Síndrome de Wolff-Parkinson-White / Cardiomiopatía Hipertrófica / Prevalencia / Muerte Súbita Cardíaca / Muerte Súbita / Ventrículos Cardíacos / Hidrocefalia / Hipertrofia / Miocardio Tipo de estudio: Estudio de prevalencia Límite: Adolescente / Humanos Idioma: Coreano Revista: Journal of the Korean Pediatric Cardiology Society Año: 2004 Tipo del documento: Artículo

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Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Taquicardia / Síndrome de Wolff-Parkinson-White / Cardiomiopatía Hipertrófica / Prevalencia / Muerte Súbita Cardíaca / Muerte Súbita / Ventrículos Cardíacos / Hidrocefalia / Hipertrofia / Miocardio Tipo de estudio: Estudio de prevalencia Límite: Adolescente / Humanos Idioma: Coreano Revista: Journal of the Korean Pediatric Cardiology Society Año: 2004 Tipo del documento: Artículo