The perioperative management of a patient with lowe syndrome for general anesthesia: A case report / 대한마취과학회지
Korean Journal of Anesthesiology
;
: 112-115, 2009.
Artículo
en Coreano
| WPRIM
| ID: wpr-22026
ABSTRACT
Lowe syndrome (the oculo-cerebro-renal syndrome of Lowe, OCRL) is a multi-system disorder that affects the eyes, nervous system, and kidney. OCRL is a rare X-linked recessive disease with a prevalence of approximately 1 500,000. The clinical features of OCRL include congenital cataracts, growth and mental retardation, areflexia, hypotonia, and renal tubular dysfunction (Fanconi-type). Chronic metabolic acidosis and hypotonia may be the most important component affecting management of the peri-anesthetic period during general anesthesia. However, problems such as electrolyte imbalance, seizure, fragility of the bone structures, and increased intraocular pressure should also be considered during the perioperative period. We report here the perioperative management of a patient with Lowe syndrome during the removal of multiple scalp cysts under general anesthesia.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Cuero Cabelludo
/
Convulsiones
/
Acidosis
/
Catarata
/
Prevalencia
/
Ojo
/
Periodo Perioperatorio
/
Presión Intraocular
/
Anestesia General
/
Riñón
Tipo de estudio:
Estudio de prevalencia
Límite:
Humanos
Idioma:
Coreano
Revista:
Korean Journal of Anesthesiology
Año:
2009
Tipo del documento:
Artículo
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