Pulmonary hypertension in a child with juvenile-type autosomal recessive polycystic kidney disease
Journal of Korean Medical Science
; : 451-454, 1999.
Article
en En
| WPRIM
| ID: wpr-221955
Biblioteca responsable:
WPRO
ABSTRACT
An 11 year-old girl, whose condition was diagnosed as juvenile-type autosomal recessive polycystic kidney disease (ARPKD) at five years of age, presented with chest pain and dyspnea that had developed suddenly two months previously. Two-dimensional echocardiography, Doppler study and cardiac catheterization confirmed pulmonary hypertension. The underlying mechanism of the diagnosis was not defined. Two and a half months after the onset of symptoms, the patient died of pulmonary hypertensive crisis. Careful regular checks of cardiopulmonary status using two-dimensional echocardiography and Doppler should be considered for the early detection of pulmonary hypertension even in an asymptomatic patient with juvenile-type ARPKD.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Biopsia
/
Ecocardiografía Doppler
/
Riñón Poliquístico Autosómico Recesivo
/
Resultado Fatal
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Hipertensión Pulmonar
/
Cirrosis Hepática
Tipo de estudio:
Screening_studies
Límite:
Child
/
Female
/
Humans
Idioma:
En
Revista:
Journal of Korean Medical Science
Año:
1999
Tipo del documento:
Article